Thread by @ladiologist

31yo F, brother sudden cardiac death at 34yo, father sudden cardiac death at 45yo

Should she be worried??

#radtwitter #medtwitter #cardiotwitter #whyCMR

Patient also had basal septal hypertrophy up to 21mm (left), associated with delayed enhancement (right)

Dad was thought to have died from MI. Brother had suspicion of ARVD on echo, died before CMR, no autopsy. Her CMR was requested to rule out ARVD.

Her findings are consistent with hypertrophic obstructive cardiomyopathy (HOCM). The 3-chamber cine shows LVOT gradient and near complete obstruction in systole, all @ the site of the hypertrophied basal septum. SAM was present w/ MR. She will be considered for ICD and myomectomy