-congenital defect in posterior diaphragm attachment
- Can be either side (classic =L side in symptomatic infants➡️lung hypoplasia, but R m/c in adults?)
- typically only fat but ~25% can contain abd organs
#WetreadCoW Case 11 Answer: Pseudomyxoma Peritonei
-accumulation of mucinous ascites from mucin producing tumor. This case is the classic mucinous appendiceal tumor s/p multiple debulking surgeries! #FOAMed#FOAMrad#Radres#bodyrad
-seroneg spondyloarthropathy (neg Rheum factor) ➡️ fusion of the spine, SI jts, pubic symphsysis, and sometimes other jts
- assoc w HLA B27 gene
-M>F
-usually presents 3rd-4th decade
-trt: NSAIDS, motion/exercise, TNF-alpha blockers